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Chapter III

Other hereditary haemolytic anaemias - D58


D58.0 Hereditary spherocytosis
Acholuric (familial) jaundice
Congenital (spherocytic) haemolytic icterus
Minkowski-Chauffard syndrome
D58.1 Hereditary elliptocytosis
Elliptocytosis (congenital)
Ovalocytosis (congenital)(hereditary)
D58.2 Other haemoglobinopathies
Abnormal haemoglobin NOS
Congenital Heinz body anaemia
Disease:
· Hb-C
· Hb-D
· Hb-E
Haemoglobinopathy NOS
Unstable haemoglobin haemolytic disease
    Excludes:
  • familial polycythaemia ( D75.0 )
  • Hb-M disease ( D74.0 )
  • hereditary persistence of fetal haemoglobin [HPFH] ( D56.4 )
  • high-altitude polycythaemia ( D75.1 )
  • methaemoglobinaemia ( D74.- )
D58.8 Other specified hereditary haemolytic anaemias
Stomatocytosis
D58.9 Hereditary haemolytic anaemia, unspecified


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