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Chapter IV

Other disorders of carbohydrate metabolism - E74


    Excludes:
  • increased secretion of glucagon ( E16.3 )
  • diabetes mellitus ( E10-E14 )
  • hypoglycaemia NOS ( E16.2 )
  • mucopolysaccharidosis ( E76.0-E76.3 )
E74.0 Glycogen storage disease
Cardiac glycogenosis
Disease:
· Andersen
· Cori
· Forbes
· Hers
· McArdle
· Pompe
· Tauri
· von Gierke
Liver phosphorylase deficiency
E74.1 Disorders of fructose metabolism
Essential fructosuria
Fructose-1,6-diphosphatase deficiency
Hereditary fructose intolerance
E74.2 Disorders of galactose metabolism
Galactokinase deficiency
Galactosaemia
E74.3 Other disorders of intestinal carbohydrate absorption
Glucose-galactose malabsorption
Sucrase deficiency
    Excludes:
  • lactose intolerance ( E73.- )
E74.4 Disorders of pyruvate metabolism and gluconeogenesis
Deficiency of:
· phosphoenolpyruvate carboxykinase
· pyruvate:
  · carboxylase
  · dehydrogenase
    Excludes:
  • with anaemia ( D55.- )
E74.8 Other specified disorders of carbohydrate metabolism
Essential pentosuria
Oxalosis
Oxaluria
Renal glycosuria
E74.9 Disorder of carbohydrate metabolism, unspecified


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