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Chapter IV

Disorders of lipoprotein metabolism and other lipidaemias - E78


    Excludes:
  • sphingolipidosis ( E75.0-E75.3 )
E78.0 Pure hypercholesterolaemia
Familial hypercholesterolaemia
Fredrickson's hyperlipoproteinaemia, type IIa
Hyperbetalipoproteinaemia
Hyperlipidaemia, group A
Low-density-lipoprotein-type [LDL] hyperlipoproteinaemia
E78.1 Pure hyperglyceridaemia
Endogenous hyperglyceridaemia
Fredrickson's hyperlipoproteinaemia, type IV
Hyperlipidaemia, group B
Hyperprebetalipoproteinaemia
Very-low-density-lipoprotein-type [VLDL] hyperlipoproteinaemia
E78.2 Mixed hyperlipidaemia
Broad- or floating-betalipoproteinaemia
Fredrickson's hyperlipoproteinaemia, type IIb or III
Hyperbetalipoproteinaemia with prebetalipoproteinaemia
Hypercholesterolaemia with endogenous hyperglyceridaemia
Hyperlipidaemia, group C
Tubero-eruptive xanthoma
Xanthoma tuberosum
    Excludes:
  • cerebrotendinous cholesterosis [van Bogaert-Scherer-Epstein] ( E75.5 )
E78.3 Hyperchylomicronaemia
Fredrickson's hyperlipoproteinaemia, type I or V
Hyperlipidaemia, group D
Mixed hyperglyceridaemia
E78.4 Other hyperlipidaemia
Familial combined hyperlipidaemia
E78.5 Hyperlipidaemia, unspecified
E78.6 Lipoprotein deficiency
Abetalipoproteinaemia
High-density lipoprotein deficiency
Hypoalphalipoproteinaemia
Hypobetalipoproteinaemia (familial)
Lecithin cholesterol acyltransferase deficiency
Tangier disease
E78.8 Other disorders of lipoprotein metabolism
E78.9 Disorder of lipoprotein metabolism, unspecified


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