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Chapter XVII

Congenital malformations of great arteries - Q25


Q25.0 Patent ductus arteriosus
Patent ductus Botallo
Persistent ductus arteriosus
Q25.1 Coarctation of aorta
Coarctation of aorta (preductal)(postductal)
Q25.2 Atresia of aorta
Q25.3 Stenosis of aorta
Supravalvular aortic stenosis
    Excludes:
  • congenital aortic stenosis ( Q23.0 )
Q25.4 Other congenital malformations of aorta
of aorta:
Absence
Aplasia
Congenital:
· aneurysm
· dilatation

Aneurysm of sinus of Valsalva (ruptured)
Double aortic arch [vascular ring of aorta]
Hypoplasia of aorta
Persistent:
· convolutions of aortic arch
· right aortic arch
    Excludes:
  • hypoplasia of aorta in hypoplastic left heart syndrome ( Q23.4 )
Q25.5 Atresia of pulmonary artery
Q25.6 Stenosis of pulmonary artery
Q25.7 Other congenital malformations of pulmonary artery
Aberrant pulmonary artery
Agenesis
Aneurysm, congenital
Anomaly
Hypoplasia

Pulmonary arteriovenous aneurysm
Q25.8 Other congenital malformations of great arteries
Q25.9 Congenital malformation of great arteries, unspecified


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