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Chapter XVII

Other congenital malformations of skin - Q82


    Excludes:
  • acrodermatitis enteropathica ( E83.2 )
  • congenital erythropoietic porphyria ( E80.0 )
  • pilonidal cyst or sinus ( L05.- )
  • Sturge-Weber(-Dimitri) syndrome ( Q85.8 )
Q82.0 Hereditary lymphoedema
Q82.1 Xeroderma pigmentosum
Q82.2 Mastocytosis
Urticaria pigmentosa
    Excludes:
  • malignant mastocytosis ( C96.2 )
Q82.3 Incontinentia pigmenti
Q82.4 Ectodermal dysplasia (anhidrotic)
    Excludes:
  • Ellis-van Creveld syndrome ( Q77.6 )
Q82.5 Congenital non-neoplastic naevus
Birthmark NOS
Naevus:
· flammeus
· portwine
· sanguineous
· strawberry
· vascular NOS
· verrucous
    Excludes:
  • cafe au lait spots ( L81.3 )
  • lentigo ( L81.4 )
  • naevus:
    · NOS ( D22.- )
    · araneus ( I78.1 )
    · melanocytic ( D22.- )
    · pigmented ( D22.- )
    · spider ( I78.1 )
    · stellar ( I78.1 )
Q82.8 Other specified congenital malformations of skin
Abnormal palmar creases
Accessory skin tags
Benign familial pemphigus [Hailey-Hailey]
Cutis laxa (hyperelastica)
Dermatoglyphic anomalies
Inherited keratosis palmaris et plantaris
Keratosis follicularis [Darier-White]
    Excludes:
  • Ehlers-Danlos syndrome ( Q79.6 )
Q82.9 Congenital malformation of skin, unspecified


Related drugs:
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