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Chapter III

Immunodeficiency with predominantly antibody defects - D80


D80.0 Hereditary hypogammaglobulinaemia
Autosomal recessive agammaglobulinaemia (Swiss type)
X-linked agammaglobulinaemia [Bruton] (with growth hormone deficiency)
D80.1 Nonfamilial hypogammaglobulinaemia
Agammaglobulinaemia with immunoglobulin-bearing B-lymphocytes
Common variable agammaglobulinaemia [CVAgamma]
Hypogammaglobulinaemia NOS
D80.2 Selective deficiency of immunoglobulin A [IgA]
D80.3 Selective deficiency of immunoglobulin G [IgG] subclasses
D80.4 Selective deficiency of immunoglobulin M [IgM]
D80.5 Immunodeficiency with increased immunoglobulin M [IgM]
D80.6 Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinaemia
D80.7 Transient hypogammaglobulinaemia of infancy
D80.8 Other immunodeficiencies with predominantly antibody defects
Kappa light chain deficiency
D80.9 Immunodeficiency with predominantly antibody defects, unspecified


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