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Chapter III

Combined immunodeficiencies - D81


    Excludes:
  • autosomal recessive agammaglobulinaemia (Swiss type) ( D80.0 )
D81.0 Severe combined immunodeficiency [SCID] with reticular dysgenesis
D81.1 Severe combined immunodeficiency [SCID] with low T- and B-cell numbers
D81.2 Severe combined immunodeficiency [SCID] with low or normal B-cell numbers
D81.3 Adenosine deaminase [ADA] deficiency
D81.4 Nezelof's syndrome
D81.5 Purine nucleoside phosphorylase [PNP] deficiency
D81.6 Major histocompatibility complex class I deficiency
Bare lymphocyte syndrome
D81.7 Major histocompatibility complex class II deficiency
D81.8 Other combined immunodeficiencies
Biotin-dependent carboxylase deficiency
D81.9 Combined immunodeficiency, unspecified
Severe combined immunodeficiency disorder [SCID] NOS


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