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Chapter IV

Other disorders of carbohydrate metabolism - E74


    Excludes:
  • increased secretion of glucagon ( E16.3 )
  • diabetes mellitus ( E10-E14 )
  • hypoglycaemia NOS ( E16.2 )
  • mucopolysaccharidosis ( E76.0-E76.3 )
E74.0 Glycogen storage disease
Cardiac glycogenosis
Disease:
  • Andersen
  • Cori
  • Forbes
  • Hers
  • McArdle
  • Pompe
  • Tauri
  • von Gierke
    Liver phosphorylase deficiency
  • E74.1 Disorders of fructose metabolism
    Essential fructosuria
    Fructose-1,6-diphosphatase deficiency
    Hereditary fructose intolerance
    E74.2 Disorders of galactose metabolism
    Galactokinase deficiency
    Galactosaemia
    E74.3 Other disorders of intestinal carbohydrate absorption
    Glucose-galactose malabsorption
    Sucrase deficiency
      Excludes:
    • lactose intolerance ( E73.- )
    E74.4 Disorders of pyruvate metabolism and gluconeogenesis
    Deficiency of:
  • phosphoenolpyruvate carboxykinase
  • pyruvate:
      
  • carboxylase
      
  • dehydrogenase
      Excludes:
    • with anaemia ( D55.- )
  • E74.8 Other specified disorders of carbohydrate metabolism
    Essential pentosuria
    Oxalosis
    Oxaluria
    Renal glycosuria
    E74.9 Disorder of carbohydrate metabolism, unspecified


    Related drugs:
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