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Chapter IV

Disorders of glycosaminoglycan metabolism - E76


E76.0 Mucopolysaccharidosis, type I
Syndrome:
  • Hurler
  • Hurler-Scheie
  • Scheie
  • E76.1 Mucopolysaccharidosis, type II
    Hunter's syndrome
    E76.2 Other mucopolysaccharidoses
    Beta-glucuronidase deficiency
    Mucopolysaccharidosis, types III, IV, VI, VII
    Syndrome:
  • Maroteaux-Lamy (mild)(severe)
  • Morquio(-like)(classic)
  • Sanfilippo (type B)(type C)(type D)
  • E76.3 Mucopolysaccharidosis, unspecified
    E76.8 Other disorders of glucosaminoglycan metabolism
    E76.9 Disorder of glucosaminoglycan metabolism, unspecified


    Related drugs:
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